casepresentationjune25,20xx内容摘要:
Factor XIIa Factor XII Factor XIIa Prekallikrein Kallikrein HK Bradykinin Factor XIIf C1 C1 C4, C2 digestion Surface Surface Inhibited By C1 INH Plasmin Plasminogen Further Data Regarding C1 INH Complete acid sequence known。 heavily glycosylated Generation of cDNA clones acplished, localization to chromosome 11 Deficiency heterogeneous by DNA restriction fragment length polymorphisms Deficiency frequently associated with autoimmune phenomena Mechanisms of acquired C1 inhibitor deficiency: Depletion by plement activation Contact system activation AntiC1 inhibitor antibodies Antiidi。casepresentationjune25,20xx
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