casepresentationjune25,20xx内容摘要:

Factor XIIa Factor XII Factor XIIa Prekallikrein Kallikrein HK Bradykinin Factor XIIf C1 C1 C4, C2 digestion Surface Surface Inhibited By C1 INH Plasmin Plasminogen Further Data Regarding C1 INH  Complete acid sequence known。 heavily glycosylated  Generation of cDNA clones acplished, localization to chromosome 11  Deficiency heterogeneous by DNA restriction fragment length polymorphisms  Deficiency frequently associated with autoimmune phenomena  Mechanisms of acquired C1 inhibitor deficiency:  Depletion by plement activation  Contact system activation  AntiC1 inhibitor antibodies  Antiidi。
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